Involuntary Bickerstaff Brainstem Encephalitis Movements Mimicking anti-NMDA Receptor Encephalitis
Bickerstaff brainstem encephalitis (BBE) is a rare autoimmune neurological disease characterized by a triad of acute eye muscle weakness (ophthalmoplegia), ataxia, and altered consciousness, with positive serum IgG anti-GQ1b and negative anti-N-methyl-D-aspartate (NMDA) receptor antibodies.
[0:00] This video shows an unusual manifestation of the disorder in a previously healthy 20-year-old woman.
[0:03]: On day 1, the patient presented with bilateral ptosis, severe external ophthalmoplegia in all eye muscles, and facial grimacing and sniffing motions.
[0:29]: By day 5, she developed slow and restless movements in her lower limbs and rapid neck twisting.
[0:56]: On day 7, abnormal movements appeared in her upper limbs, and her consciousness disturbance and ophthalmoplegia improved.
The abnormal movements are unusual for BBE and are more characteristic of anti-NMDA encephalitis. The patient returned to normal after treatment with intravenous immunoglobulin and methylprednisolone.
Click https://ja.ma/2TJndMF for full case details and discussion.
Видео Involuntary Bickerstaff Brainstem Encephalitis Movements Mimicking anti-NMDA Receptor Encephalitis канала JAMA Network
[0:00] This video shows an unusual manifestation of the disorder in a previously healthy 20-year-old woman.
[0:03]: On day 1, the patient presented with bilateral ptosis, severe external ophthalmoplegia in all eye muscles, and facial grimacing and sniffing motions.
[0:29]: By day 5, she developed slow and restless movements in her lower limbs and rapid neck twisting.
[0:56]: On day 7, abnormal movements appeared in her upper limbs, and her consciousness disturbance and ophthalmoplegia improved.
The abnormal movements are unusual for BBE and are more characteristic of anti-NMDA encephalitis. The patient returned to normal after treatment with intravenous immunoglobulin and methylprednisolone.
Click https://ja.ma/2TJndMF for full case details and discussion.
Видео Involuntary Bickerstaff Brainstem Encephalitis Movements Mimicking anti-NMDA Receptor Encephalitis канала JAMA Network
Показать
Комментарии отсутствуют
Информация о видео
Другие видео канала
![Susannah Cahalan's Month of Madness](https://i.ytimg.com/vi/Najj0aVLJwU/default.jpg)
![AIDP: Guillain-Barre, Miller-Fisher, and Bickerstaff’s Brainstem Encephalitis](https://i.ytimg.com/vi/cdBbRN_Q1TU/default.jpg)
![N-methyl-d-aspartate Receptor Autoimmune Encephalitis Presenting With Opsoclonus-Myoclonus: Treatmen](https://i.ytimg.com/vi/qdnNDnJki6M/default.jpg)
![Teratoma-Induced Anti–NMDA Receptor Encephalitis](https://i.ytimg.com/vi/OyPgb6V08ok/default.jpg)
![“Brain on Fire” Condition Explained: What is Anti-NMDA Receptor Encephalitis?](https://i.ytimg.com/vi/wPJmTls6vEU/default.jpg)
![Encephalitis - My Brain: My Story 2019 - Mallory's Story](https://i.ytimg.com/vi/Nk6Pp2ZaOhQ/default.jpg)
![Encephalitis (“Brain Inflammation”) Signs and Symptoms (& Why They Occur)](https://i.ytimg.com/vi/oQCmjX33pLI/default.jpg)
![Fatal Autoimmune anti-NMDA-receptor Encephalitis - Supplementary video [ID 311071]](https://i.ytimg.com/vi/Eg5Wg8pC1fY/default.jpg)
![Overcoming Anti-NMDA Receptor Encephalitis - Mayo Clinic](https://i.ytimg.com/vi/tK2Ka49GS7M/default.jpg)
![Vennada's Story: Recovery from Anti-NMDA Receptor Encephalitis](https://i.ytimg.com/vi/s3H2w23HDhw/default.jpg)
![What is Anti-NMDAR Encephalitis?](https://i.ytimg.com/vi/Jf9QH7ax26w/default.jpg)
![Clinical Pearls in Autoimmune Encephalopathy - Eoin Flanagan, M.D.](https://i.ytimg.com/vi/8PAX1QwYx8A/default.jpg)
![Anti NMDA Receptor Encephalitis - Amanda's Rare Autoimmune Disease Story](https://i.ytimg.com/vi/Ptj8JrqgcG4/default.jpg)
![Autoimmune Encephalitis ~Recognizing signs at onset, Diagnosis and Treatment](https://i.ytimg.com/vi/BCpSs8qdvds/default.jpg)
![Neurology Grand Rounds- Brain on Fire & Other Lessons of Autoimmune Encephalitis- Pavel Repovic, MD](https://i.ytimg.com/vi/Ds5oYINeJGE/default.jpg)
![Brain on Fire: Laura's Journey with Autoimmune Encephalitis](https://i.ytimg.com/vi/w41SWAXS-Bk/default.jpg)
![Anti-NMDA Receptor Encephalitis: "Brain on Fire"](https://i.ytimg.com/vi/sqn3zYwJ62E/default.jpg)
![Imaging CNS autoimmune and inflammatory disease - 1 - Introduction/Demyelinating disease](https://i.ytimg.com/vi/ONjHU79gB3w/default.jpg)
![Anti-N-methyl-D-aspartate (Anti-NMDA) Receptor Encephalitis (Brain on Fire) – A Synopsis](https://i.ytimg.com/vi/ixvpL8SxGoE/default.jpg)
![Autoimmune Encephalitis Alliance: You are not alone](https://i.ytimg.com/vi/5YcqEKAAj4U/default.jpg)